| CASE REPORT |
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| Year : 2023 | Volume
: 3
| Issue : 2 | Page : 93-95 |
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Bart Syndrome: A Deceptively Scary Presentation
Madhvi Trivedi, Rajesh Dutt Mehta, Bhikam Chand Ghiya, Prasoon Soni
Department of Dermatology, Venereology and Leprosy, Sardar Patel Medical College, Bikaner, Rajasthan, India
Correspondence Address:
Dr. Madhvi Trivedi
549, Shiva Nagar, Udaipur - 313 001, Rajasthan
India
 Source of Support: None, Conflict of Interest: None
DOI: 10.4103/ipcares.ipcares_19_23
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Background: Bart syndrome is one of the rarest forms of aplasia cutis congenita (ACC). Clinical Description: We report a sporadic case of a neonate presenting with the absence of skin on the lower limb, tense blisters on fingers, and nail dystrophy. Management: Clinical features and skin biopsy confirmed the diagnosis of Bart syndrome. The baby was given symptomatic treatment with regular antimicrobial dressing. Within 2 weeks, the defect healed with the formation of hypopigmented scar and milia. The bullous lesions also disappeared completely. Conclusion: Bart syndrome, which is a type of ACC, is an extremely rare occurrence. Although it has an extensive involvement, the lesions if superficial, limited to the epidermis, have a good prognosis. Conservative management is sufficient to cause healing within a short span of time. |
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